NSTL国家科技图书文献中心

1. A solitary scalp mass as the presenting feature of clear cell sarcoma of the kidney in a pediatric patient NSTL国家科技图书文献中心

Pascual, Micah G. | Bruckner, Anna L.... - 《Pediatric dermatology》 - 2024,41(4) - 684～687 - 共4页

摘要：Clear cell sarcoma of the kidney is a rare renal malignancy, accounting for 2%-4% of all pediatric renal tumors. In this case report, we describe a 9-year-old boy with an asymptomatic, solitary mass o...

关键词： case report | clear cell sarcoma of the kidney | pilar cyst | proliferating pilar cyst | scalp mass | CALVARIAL MASSES | SKULL | CHILDREN | INFANTS | LESIONS

2. Efficacy and safety of Oleogel-S10 (birch triterpenes) for epidermolysis bullosa: results from the phase III randomized double-blind phase of the EASE study NSTL国家科技图书文献中心

Kern, Johannes S. | Sprecher, Eli ... - 《British Journal of Dermatology》 - 2023,188(1) - 12～21 - 共10页 - 被引量：18

摘要：Background Epidermolysis bullosa (EB) is a heterogeneous group of rare, difficult-to-treat, inherited multisystem diseases affecting epithelial integrity. Patients with EB are affected by mechanical f...

关键词： SCARRING INDEX EBDASI | DISEASE-ACTIVITY | PREVALENCE | INSTRUMENT

3. Assessing pain catastrophizing and functional disability in pediatric epidermolysis bullosa patients NSTL国家科技图书文献中心

Rangu, Sneha | Collins, Jessica ... - 《Pediatric dermatology》 - 2023,40(3) - 422～427 - 共6页 - 被引量：1

摘要：Background/Objectives: The primary objective was to assess pain catastrophizing and functional disability in pediatric patients with epidermolysis bullosa (EB) and their parents/guardians. Secondary o...

关键词： children | epidermolysis bullosa | pain | pediatric dermatology | pediatric psychology | CHILDREN | YOUTH

4. Anesthetic Management and Outcomes of Patients With Epidermolysis Bullosa: Experience at a Tertiary Referral Center SCIE Web of Science核心 NSTL国家科技图书文献中心

Peterson, Melissa Br... | Strupp, Kim M.... - 《Anesthesia and Analgesia: Journal of the International Anesthesia Research Society》 - 2022,134(4) - 810～821 - 共12页 - 被引量：2

摘要：BACKGROUND: Epidermolysis bullosa (EB) is a group of rare epithelial disorders caused by abnormal or absent structural proteins at the epidermal-dermal junction. As a result, patients experience blist...

关键词： CUMULATIVE EXPERIENCE | PEDIATRIC-PATIENTS | PAIN MANAGEMENT | COMPLICATIONS | CHILDREN | INTUBATION | CARE | DIFFICULT | REGISTRY

5. Milestones 2.0: An advancement in competency-based assessment for dermatology NSTL国家科技图书文献中心

Motaparthi, Kiran | Edgar, Laura ... - 《Clinics in dermatology》 - 2022,40(6) - 776～781 - 共6页

摘要：In 2013, Next Accreditation System and Milestones became the competency-based assessment framework required for all specialties accredited by the Accreditation Council for Graduate Medical Ed-ucation....

关键词： ACCREDITATION

6. Consensus recommendations for the use of retinoids in ichthyosis and other disorders of cornification in children and adolescents SCOPUS Scopus数据库 SCIE Web of Science核心 NSTL国家科技图书文献中心

Zaenglein, Andrea L. | Levy, Moise L.... - 《Pediatric dermatology》 - 2021,38(1) - 164～180 - 共17页 - 被引量：21

摘要：Topical and systemic retinoids have long been used in the treatment of ichthyoses and other disorders of cornification. Due to the need for long-term use of retinoids for these disorders, often beginn...

关键词： retinoid | ichthyosis | disorder of cornification | systemic therapy | topical therapy | adverse drug effects | drug monitoring | safety monitoring | bone health | hyperlipidemia...

7. Characterization of wound microbes in epidermolysis bullosa: Results from the epidermolysis bullosa clinical characterization and outcomes database NSTL国家科技图书文献中心

Levin, Laura E. | Shayegan, Leila H.... - 《Pediatric dermatology》 - 2021,38(1) - 119～124 - 共6页 - 被引量：11

摘要：Background/Objectives Patients with epidermolysis bullosa (EB) require care of wounds that are colonized or infected with bacteria. A subset of EB patients are at risk for squamous cell carcinoma, and...

关键词： cultures | epidermolysis bullosa | microbes | resistance | wound

8. Ancestral patterns of recessive dystrophic epidermolysis bullosa mutations in Hispanic populations suggest sephardic ancestry NSTL国家科技图书文献中心

Warshauer, Emily Mir... | Brown, Adam ... - 《American journal of medical genetics, Part A》 - 2021,185A(11) - 3390～3400 - 共11页 - 被引量：3

摘要：Recessive dystrophic epidermolysis bullosa (RDEB) is a rare genodermatosis caused by mutations in the gene coding for type VII collagen (COL7A1). More than 800 different pathogenic mutations in COL7A1...

关键词： epidermolysis bullosa | genetics | genodermatoses

9. Online education improves pediatric residents' understanding of atopic dermatitis SCOPUS Scopus数据库 SCIE Web of Science核心 NSTL国家科技图书文献中心

Craddock, Megan F. | Blondin, Heather M.... - 《Pediatric dermatology》 - 2018,35(1) - 64～69 - 共6页 - 被引量：6

摘要：Background/ObjectivesPediatricians manage skin conditions such as atopic dermatitis (AD) but report that their dermatologic training is inadequate. Online modules may enhance medical education when su...

关键词： atopic dermatitis | dermatology | online education | pediatric residency

10. Approach and Safety of Esophageal Dilation for Treatment of Strictures in Children With Epidermolysis Bullosa NSTL国家科技图书文献中心

Anderson, Bradley T. | Feinstein, James A.... - 《Journal of pediatric gastroenterology and nutrition》 - 2018,67(6) - 701～705 - 共5页 - 被引量：4

摘要：Objective: The aim of the study is to analyze a large series of esophageal balloon dilations in patients with epidermolysis bullosa (EB) to determine procedural approach and frequency of post-endoscop...